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עמוד בית
Thu, 03.04.25

Familial Mediterranean Fever

IMAJ | volume 13

Journal 4, April 2011
pages: -

Atypical Henoch-Schonlein Purpura: A Forerunner of Familial Mediterranean Fever

    Summary

    Intussuception is the most common cause of intestinal obstruction in early childhood. The cause of most intussusceptions is unknown but it can complicate the course of Henoch-Schonlein purpura (HSP) as a result of the vasculitic process. Familial Mediterranean fever (FMF), a most common disease in Israel is also associated with HSP. In a few patients, particularly in children, HSP has been reported to precede the diagnosis of FMF. We describe two patients with an unusual clinical course of severe abdominal pain as a result of intusucception. The correlation between intusucception, HSP and FMF are discussed.

     

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